Porphobilinogen deaminase over-expression in hepatocytes, but not in erythrocytes, prevents accumulation of toxic porphyrin precursors in a mouse model of acute intermittent porphyria
Author:
Carmen Unzu,Ana Sampedro,Itsaso Mauleón,Lucía Vanrell,Juan Dubrot,Rafael Enríquez de Salamanca,Gloria González-Aseguinolaza,Ignacio Melero,Jesús Prieto,Antonio Fontanellas
Publication:
Journal of Hepatology
Copyright © 2009 European Association for the Study of the Liver. Published by Elsevier B.V. All rights reserved.